Results of plate osteosynthesis of the femur at the patient with osteogenesis imperfecta
K. V. Shevyrev, 
D. A. Shavyrin,
D. V. Martynenko,
E. V. Proskurina,
V. P. Voloshin,
R. V. Kondaleva,
M. A. Shakhova
D. A. Shavyrin,
D. V. Martynenko,
E. V. Proskurina,
V. P. Voloshin,
R. V. Kondaleva,
M. A. Shakhova https://doi.org/10.14341/osteo13189
Abstract
Osteogenesis imperfecta is a rare disease characterized by bone fragility, frequent fractures, bone deformities, and low bone mineral density. The relative risk of bone fractures in patients with osteogenesis imperfecta is 4–6 times higher than in the general population. In adult patients with osteogenesis imperfecta, the incidence of femoral shaft fractures is approximately 35 times higher than in the general population. According to modern literature data, the preferred method of osteosynthesis in such patients is intramedullary. Osteosynthesis with plates is associated with a high incidence of complications. A case of treatment of a patient with osteogenesis imperfecta who underwent two femoral osteosynthesis operations with plates at an interval of 2.5 years is presented. The first operation was performed for a femoral shaft fracture at the height of varus deformity. The second osteosynthesis was performed for a peri-implant fracture of the proximal femur. Femoral consolidation was achieved at both levels. The presented case demonstrates that plate osteosynthesis can be effective in the treatment of femoral fractures in patients with osteogenesis imperfecta, achieving consolidation if the described surgical nuances are observed
About the Authors
K. V. Shevyrev
Moscow regional clinical and research institute by M.F. Vladimirsky
Russian Federation
Competing Interests:
Russian Federation
Konstantin V. Shevyrev, MD, Cand. Sci. (Med.)
Shchepkina St., 61/2 Moscow, 129110
Competing Interests:
none
D. A. Shavyrin
Moscow regional clinical and research institute by M.F. Vladimirsky
Russian Federation
Competing Interests:
Russian Federation
Dmitriy A. Shavyrin, MD, Dr. Sci. (Med.)
Shchepkina St., 61/2 Moscow, 129110
Competing Interests:
none
D. V. Martynenko
Moscow regional clinical and research institute by M.F. Vladimirsky
Russian Federation
Competing Interests:
Russian Federation
Dmitriy V. Martynenko, MD, Cand. Sci. (Med.), associate professor
Shchepkina St., 61/2 Moscow, 129110
Competing Interests:
none
E. V. Proskurina
Moscow regional clinical and research institute by M.F. Vladimirsky
Russian Federation
Competing Interests:
Russian Federation
Elena V. Proskurina
Shchepkina St., 61/2 Moscow, 129110
Competing Interests:
none
V. P. Voloshin
Moscow regional clinical and research institute by M.F. Vladimirsky
Russian Federation
Competing Interests:
Russian Federation
Victor P. Voloshin, MD, Dr. Sci. (Med.), Prof.]
Shchepkina St., 61/2 Moscow, 129110
Competing Interests:
none
R. V. Kondaleva
Moscow regional clinical and research institute by M.F. Vladimirsky
Russian Federation
Competing Interests:
Russian Federation
Regina V. Kondaleva
Shchepkina St., 61/2 Moscow, 129110
Competing Interests:
none
M. A. Shakhova
Moscow regional clinical and research institute by M.F. Vladimirsky
Russian Federation
Competing Interests:
Russian Federation
Margarita A. Shakhova
Shchepkina St., 61/2 Moscow, 129110
Competing Interests:
none
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1. Рисунок 1. Рентгенограммы пациентки с переломом правой бедренной кости. | |
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2. Рисунок 2. Рентгенограммы пациентки после остеосинтеза бедренной кости, блокируемой пластиной. | |
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3. Рисунок 3. Рентгенограммы пациентки с периимплантным переломом бедренной кости. | |
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4. Рисунок 4. Рентгенограммы пациентки после операции удаления имплантатов, корригирующей остеотомии проксимального отдела правой бедренной кости и остеосинтеза блокируемой пластиной. | |
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5. Рисунок 5. МСКТ-срезы правой бедренной кости пациентки через полгода после операции с признаками периостального мозолеобразования. | |
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6. Рисунок 6. Внешний вид пациентки через 5 лет и 4 месяца после оперативного вмешательства на правом бедре. | |
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7. Рисунок 7. Рентгенограммы правой бедренной кости пациентки 5 лет и 4 месяца после оперативного вмешательства. | |
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8. Рисунок 8. Осевые рентгенограммы нижних конечностей через 5 лет и 4 месяца после оперативного вмешательства на правом бедре. | |
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Review
For citations:
Shevyrev K.V., Shavyrin D.A., Martynenko D.V., Proskurina E.V., Voloshin V.P., Kondaleva R.V., Shakhova M.A. Results of plate osteosynthesis of the femur at the patient with osteogenesis imperfecta. Osteoporosis and Bone Diseases. 2025;28(1):38-47. (In Russ.) https://doi.org/10.14341/osteo13189
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